Overview Microscopic polyangiitis like Wegener's but lacks granulomas p-ANCA Primary pauci-immune crescentic glomerulonephritis vasculitis limited to kidney "pauci"-immune = "paucity" of antibodies Churg-Strauss syndrome granulomatous vasculitis with eosiniophilia most often presents with asthma, sinusitis, skin lesions, and peripheral neuropathy (e.g. wrist/foot drop) can also involve heart, GI, and kidneys p-ANCA All affect small vessels