Review Question - QID 109212

A 13-year-old female presents to the emergency room complaining of severe abdominal pain. She reports acute onset of diffuse abdominal pain twelve hours prior to presentation. She has vomited twice and has not had a bowel movement in that time. She is in the fetal position because it relieves the pain. Her past medical history is notable for asthma; however, she was adopted as a baby and her family history is unknown. Her temperature is 99.7°F (37.6°C), blood pressure is 130/85 mmHg, pulse is 110/min, and respirations are 22/min. Physical examination reveals abdominal distension and tenderness to palpation. A sausage-shaped abdominal mass is palpated in the right upper quadrant. Mucocutaneous blue-gray macules are evident on the child’s buccal mucosa. A mutation in which of the following genes is associated with this patient’s condition?